| CASE REPORT |
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| Year : 2022 | Volume
: 10
| Issue : 1 | Page : 40-43 |
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Klippel–Trénaunay Syndrome (KTS or KT) is a rare clinical syndrome
Mahendra Kumar Gosaliya, Jitendra Aloria, Rajesh Goel, Dinesh Kumar Bairwa, Mohit Maheshwari, Sachin Pachori
Govt. Medical College & Attached Groups of Hospitals, Kota, Rajasthan, India
Correspondence Address:
Dr. Jitendra Aloria
Govt. Medical College & Attached Groups of Hospitals, Arya Hospitals near police line Sikar, Rajasthan, 332001
India
 Source of Support: None, Conflict of Interest: None
DOI: 10.4103/JOASP.JOASP_53_21
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Klippel Trenaunay syndrome is a congenital illness that affects capillary abnormalities, varicosities, and musculoskeletal hypertrophy. That condition incorporates a range of pathology, comprising haemorrhage, venous thromboembolism, embolic consequences, with, in exceptional situations, appendage elongation, which may necessitate surgery. Venous aberrations are divided into the following but never pass the centreline. Nevertheless, we encountered a scenario of an 8-year-old kid that manifested having varicosity of vasculature or deformation of the right lower extremity, as well as cavernous haemangiomas distributed everywhere in his chest, back, gluteal area, and legs since new. Due to the involvement of neurofibromatosis, several paravertebral soft tissue masses and bladder hypertrophy were also seen. In clinical practise, the coexistence of KTS with neurofibromatosis is uncommon. |
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